|
KMID : 0191120010160020245
|
|
Journal of Korean Medical Science
2001 Volume.16 No. 2 p.245 ~ p.249
|
|
|
Multiple Intracranial Aneurysms Associated with Branchio-Oto-Dysplasia
|
|
Jin Hwan Cheong
Choong Hyun Kim/Koang Hum Bak/Jae Min Kim/Suck Jun Oh
|
|
|
Abstract
|
|
|
Branchio-oto-dysplasia is characterized by abnormalities of embryonic branchial arch system
and deafness inherited as autosomal dominant with variable gene expression. We present a
rare case of multiple intracranial aneurysms associated with branchio-oto-dysplasia. A
40-yr-old man with severe headache presented as spontaneous subarachnoid hemorrhage on
brain computed tomographic scan. The patient also manifested clinical features of
branchio- oto-dysplasia and right hemifacial hypoplasia. Carotid angiogram confirmed an
aneurysm in the anterior communicating artery. Intraoperative findings demonstrated multiple
aneurysms in the anterior communicating artery and in the left posterior communicating artery,
which were clipped successfully. Postoperative course was uneventful. This condition has not
been reported previously. We also reviewed literatures to discuss whether the intracranial
aneurysm was as a coincidental finding or a part of this malformation.
|
|
|
KEYWORD
|
|
|
|
|
|
FullTexts / Linksout information
|
|
 
|
|
|
Listed journal information
|
|
    
|